2A40
Chronic myelomonocytic leukaemia
Leucemia mielomonocítica crônica
CategoryDefinition
A myelodysplastic/myeloproliferative neoplasm which is characterised by persistent monocytosis, absence of a Philadelphia chromosome and BCR/ABL1 fusion gene, fewer than 20 percent blasts in the bone marrow and blood, often myelodysplasia, and absence of PDGFRA or PDGFRB rearrangement.
Exclusions
- Myeloid/lymphoid neoplasm associated with PDGFRA rearrangement
- Myeloid neoplasm associated with PDGFRB rearrangement
Inclusions
- Chronic monocytic leukaemia
Index Terms
Chronic myelomonocytic leukaemiaCMML - [chronic myelomonocytic leukaemia]chronic myelomonocytic leukaemia without mention of remissionChronic monocytic leukaemiachronic monocytoid leukaemiaChronic myelomonocytic leukaemia in complete remissionChronic myelomonocytic leukaemia with eosinophiliaCMML - [chronic myelomonocytic leukaemia] with eosinophiliaChronic myelomonocytic leukaemia Type 1CMML-1 - [chronic myelomonocytic leukaemia Type 1]Chronic myelomonocytic leukaemia Type 2CMML-2 - [chronic myelomonocytic leukaemia Type 2]