2A41

Atypical chronic myeloid leukaemia, BCR-ABL1-negative

Leucemia mieloide crônica atípica, BCR-ABL1- negativa

Category

Definition

A myelodysplastic/myeloproliferative neoplasm characterised by the principal involvement of the neutrophil series with leukocytosis with circulating immature myeloid cells, fewer than 20 percent blasts in the bone marrow and blood, and severe dysgranulopoiesis. The neoplastic cells do not have a Philadelphia chromosome or the BCR/ABL1 fusion gene.

Index Terms

Atypical chronic myeloid leukaemia, BCR-ABL1-negativeatypical chronic myeloid leukaemiasubacute myelogenous leukaemiasubacute myeloid leukaemiasubacute myelosisAtypical chronic myeloid leukaemia, BCR-ABL-negative without mention of remissionsubacute monocytic leukaemia without mention of remissionsubacute monocytic leukaemiaAtypical chronic myeloid leukaemia, BCR-ABL1-negative in complete remission