2A85.2

Extranodal marginal zone B-cell lymphoma, primary site skin

Linfoma de células B de zona marginal extranodal, localização primária na pele

Category

Definition

A low-grade, extranodal marginal zone B-cell lymphoma of the mucosa-associated lymphoid tissue that arises from the skin. It usually presents with multifocal papular or nodular lesions in the arms or trunk. It rarely disseminates to internal organs or progresses to high grade lymphoma.

Index Terms

Extranodal marginal zone B-cell lymphoma, primary site skinPrimary cutaneous marginal zone B-cell lymphomaSALT - [skin associated lymphoid tissue-related B-cell lymphoma]