2A85.4
Lymphoplasmacytic lymphoma
Linfoma linfoplasmocítico
CategoryDefinition
Neoplasm of small B lymphocytes and plasma cells, mostly residing in the bone marrow. Frequently associated with the production of an IgM serum monoclonal protein, then called Waldenström macroglobulinemia (WM).
Exclusions
- small cell B-cell lymphoma
- Chronic lymphocytic leukaemia or small lymphocytic lymphoma
Inclusions
- primary macroglobulinaemia
- Waldenström macroglobulinaemia
- Waldenström macroglobulinaemia without mention of remission
Index Terms
Lymphoplasmacytic lymphomaWaldenström macroglobulinaemiaWaldenström macroglobulinaemia without mention of remissionidiopathic macroglobulinaemiaprimary macroglobulinaemiaLymphoplasmacytic lymphoma in complete remissionWaldenström macroglobulinaemia in complete remission