2A90.4

Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood

Linfoma sistêmico de células T positivo para vírus Epstein-Barr da infância

Category

Definition

This neoplasm of childhood is characterised by a clonal proliferation of EBV-infected T-cells with an activated cytotoxic phenotype. It can occur shortly after primary acute EBV infection or in the setting of chronic active EBV infection (CAEBV).

Index Terms

Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhoodSystemic EBV+ T-cell lymphoma of childhood