2E81.10
Disseminated lymphangiomatosis
Linfangiomatose disseminada
CategoryDefinition
A rare disorder characterised by widespread proliferation of aberrant lymphatic vessels which typically infiltrate vital organs in the thorax and abdomen.
Index Terms
Disseminated lymphangiomatosisdiffuse lymphangiomatosisDiffuse lymphatic malformation (deprecated)Kaposiform lymphangiomatosis