3A50.02
Haemoglobin H disease (– α/– – included)
Doença da hemoglobina H (– α/– – included)
CategoryDefinition
Haemoglobin H (HbH) disease is a moderate to severe form of alpha-thalassemia characterised by pronounced microcytic hypochromic haemolytic anaemia.
Index Terms
Haemoglobin H disease (– α/– – included)alpha - /- - or mutational forms of alpha-thalassaemiaAlpha thalassaemia intermedia