3A50.03

Homozygous or compound heterozygous alpha0 thalassaemia

Talassemia alfa0 composta heterozigótica ou homozigótica

Category

Definition

Hb Bart's hydrops fetalis is the most severe form of alpha-thalassemia and is almost always lethal. It is characterised by fetal onset of generalised oedema, pleural and pericardial effusions, and severe hypochromic anaemia.

Index Terms

Homozygous or compound heterozygous alpha0 thalassaemiaHb Bart's hydrops fetalisAlpha thalassaemia hydrops fetalisHaemoglobin Bart hydrops fetalis