3A50.3

Delta, delta-beta or gamma-delta-beta thalassaemia

Talassemia delta, delta-beta ou gama-delta-beta

Category

Definition

Delta-beta-thalassemia is a form of beta-thalassemia characterised by decreased or absent synthesis of the delta- and beta-globin chains with a compensatory increase in expression of fetal gamma-chain synthesis.

Index Terms

Delta, delta-beta or gamma-delta-beta thalassaemiaDelta thalassaemiaDelta-beta thalassaemiaf thalassaemiaGamma-delta-beta thalassaemiaHaemoglobin Lepore