3A51.4

Compound heterozygous sickling disorders with crisis

Transtornos falciformes heterozigotos compostos com crise

Category

Definition

Compound heterozygous sickling disorders with crisis may present with acute chest syndrome, splenic sequestration, haemolytic crisis, and pain.

Index Terms

Compound heterozygous sickling disorders with crisisSickle cell Hb-C disease with crisisHb SC disease with crisisHb S Hb C disease with crisisSickle cell Hb-C disease with crisis with acute chest syndromeSickle cell Hb-C disease with crisis with splenic sequestrationSickle cell Hb-C disease with crisis with feverSickle cell thalassaemia with crisissickle-cell beta thalassaemia with crisisthalassaemia Hb S diseasethalassaemia Hb S disease with crisisSickle cell thalassaemia with crisis with acute chest syndromeSickle cell thalassaemia with crisis with splenic sequestrationSickle cell thalassaemia with crisis with feverSickle-cell thalassaemia with vaso-occlusive pain