3B15
Inherited coagulation factor deficiency without bleeding tendency
Deficiência hereditária de fator da coagulação sem tendência hemorrágica
CategoryDefinition
A disease caused by a genetically inherited mutation leading to decreased levels of coagulation factor. This disease is characterised by decreased levels of coagulation factor without leading to increased haemorrhaging. Confirmation is by identification of decreased levels of coagulation factor in a blood sample.
Index Terms
Inherited coagulation factor deficiency without bleeding tendencyCongenital prekallikrein deficiencyCongenital high-molecular-weight kininogen deficiencyHereditary factor XII deficiencyCongenital Hageman factor deficiencycongenital factor XII deficiencyDeficiency of factor XIIfactor XII deficiency diseaseHageman defectHageman deficiencyHageman factor defectHageman factor deficiency