3B62.01

Inherited giant platelet disorder

Distúrbio hereditário das plaquetas gigantes

Category

Definition

A disease caused by genetically inherited mutations. This disease is characterised by abnormally large platelets, low platelet count and a bleeding tendency. Confirmation is by identification of mutations through genetic testing.

Index Terms

Inherited giant platelet disorderBernard-Soulier syndromegiant platelet syndromeBernard-Soulier thrombopathyMediterranean macrothrombocytopeniaMacrothrombocytopenia with mitral valve insufficiency