3B64.14
Thrombotic thrombocytopenic purpura
Púrpura trombocitopênica trombótica
CategoryDefinition
This condition is idiopathic. This condition is characterised by abnormality of blood coagulation causing extensive microscopic clots to form in the small blood vessels throughout the body resulting in low platelet count. This condition may present with seizures, hemiplegia, paresthesias, visual disturbance, and aphasia or anaemia. Confirmation is by identification of thromboses.
Index Terms
Thrombotic thrombocytopenic purpuraMoschcowitz diseaseTTP - [thrombotic thrombocytopenic purpura]Moschcowitz syndromeAcquired thrombotic thrombocytopenic purpura due to anti-ADAMTS 13 antibodiesCongenital thrombotic thrombocytopenic purpura due to ADAMTS-13 deficiencyUpshaw-Schulman syndromecongenital thrombocytopaenic purpuraGlomerular disorders in thrombotic thrombocytopenic purpuraThrombotic thrombocytopenic purpura specified as refractory