4A01.01
Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
Imunodeficiências com redução grave em pelo menos dois isotipos de imunoglobulinas séricas com número normal ou baixo de células B
CategoryDefinition
This refers to a nonfamilial type of primary immune deficiency disease characterised by a reduction in at least two serum immunoglobulin isotypes. Circulating B cells may be normal or low.
Index Terms
Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cellsnonfamilial hypogammaglobulinaemiacommon variable immune deficiencynonfamilial agammaglobulinaemiacommon variable agammaglobulinaemiaagammaglobulinaemia NOSagammaglobulinaemia antibody deficiency syndromehypogammaglobulinaemia antibody deficiency syndromeacquired agammaglobulinaemia NOSHypogammaglobulinaemia NOSAgammaglobulinaemia with immunoglobulin-bearing B-lymphocytesimmunoglobulin-bearing b-lymphocytes agammaglobulinaemia