4A41.00
Adult dermatomyositis
Dermatomiosite do adulto
CategoryDefinition
Adult dermatomyositis is a systemic inflammatory disorder affecting the skeletal muscles, the skin, and other organs. It is characterised by symmetric proximal muscle weakness, increased serum muscle enzymes, myopathic changes upon electromyography, typical histological findings on muscle biopsy, and typical dermatologic manifestations such as heliotrope rash or Gottron’s papules.
Exclusions
- Myasthenia gravis or certain specified neuromuscular junction disorders
Index Terms
Adult dermatomyositisAmyopathic dermatomyositisHypomyopathic dermatomyositisAdult dermatomyositis with calcinosisParaneoplastic dermatomyositisDermatomyositis in neoplastic disease of uncertain behaviourDermatomyositis in neoplastic disease of unknown behaviourDermatopolymyositis in neoplastic disease of uncertain behaviourDermatopolymyositis in neoplastic disease of unknown behaviourAnti-synthetase syndrome with dermatomyositisAdult dermatomyositis with overlap to nonorgan specific systemic autoimmune disordersWagner-Unverricht syndrome