4A41.01

Juvenile dermatomyositis

Dermatomiosite juvenil

Category

Definition

Juvenile dermatomyositis is the early-onset form of dermatomyositis, a systemic autoimmune inflammatory muscle disorder, characterised by proximal muscle weakness, evocative skin lesion, and systemic manifestations.

Index Terms

Juvenile dermatomyositischildhood type dermatomyositisHypomyopathic juvenile dermatomyositisJuvenile dermatomyositis with cutaneous vasculitisJuvenile dermatomyositis with lipodystrophyJuvenile dermatomyositis with myocarditisJuvenile dermatomyositis with necrotising cutaneous vasculitisAmyopathic juvenile dermatomyositisJuvenile dermatomyositis with calcinosisJuvenile dermatomyositis with overlap to nonorgan specific systemic autoimmune disordersJuvenile myositis