4A41.21
Noninflammatory inclusion body myopathy
Miopatia por corpos de inclusão não inflamatória
CategoryDefinition
Noninflammatory inclusion body myopathy (IBM) is an idiopathic muscle disorder without inflammatory exudates and expression of class I major histocompatibility complex. Rimmed vacuoles and “IBM-like” filaments without inflammatory cells are described in muscle biopsy.
Exclusions
- Myasthenia gravis or certain specified neuromuscular junction disorders
Index Terms
Noninflammatory inclusion body myopathyHereditary inclusion body myopathyHIBM - [hereditary inclusion body myositis]Desmin-related myopathy with Mallory body-like inclusionsHereditary inclusion body myopathy - joint contractures - ophthalmoplegiaInclusion body myopathy with Paget disease of bone and frontotemporal dementiaIBMPFD - [inclusion body myopathy with Paget disease of bone and frontotemporal dementia]X-linked myopathy with excess autophagyXMEA - [x-linked myopathy with excess autophagy]Sporadic inclusion body myopathy