4A42.0
Paediatric onset systemic sclerosis
Esclerose sistêmica de início na infância
CategoryDefinition
Systemic sclerosis arising before the age of 16. Involvement of internal organs is less common but arthritis and myositis are more common than in adults.
Index Terms
Paediatric onset systemic sclerosisDiffuse paediatric systemic sclerosisLimited paediatric systemic sclerosis