4A44.7

Primary angiitis of the central nervous system

Angiite primária do sistema nervoso central

Category

Definition

In primary angiitis of the central nervous system, vasculitis is limited to the central nervous system. Primary angiitis of the central nervous system is a very rare disease, and its manifestation can be mimicked by many other diseases. Patients with primary angiitis commonly show headache, waxing and waning altered mental status, and transient ischemic attack-like events. Diagnosis is often based on angiography, although brain biopsy remains the only definitive diagnostic test.

Index Terms

Primary angiitis of the central nervous systemPrimary vasculitis of the central nervous systemIsolated angiitis of the central nervous systemPACNS - [primary angiitis of the central nervous system]