4A44.91

Hypocomplementaemic urticarial vasculitis

Vasculite urticariforme hipocomplementêmica

Category

Definition

Vasculitis accompanied by urticaria and hypocomplementemia affecting small vessels (i.e., capillaries, venules, or arterioles), and associated with anti-C1q antibodies. Glomerulonephritis, arthritis, obstructive pulmonary disease, and ocular inflammation are common.(Chapel Hill Consensus Conference, 2011)

Index Terms

Hypocomplementaemic urticarial vasculitisAnti-C1q vasculitis