4A44.A2
Eosinophilic granulomatosis with polyangiitis
Poliangiite com granulomatose eosinofílica
CategoryDefinition
Eosinophil-rich and necrotizing granulomatous inflammation often involving the respiratory tract, and necrotizing vasculitis predominantly affecting small to medium-sized vessels, and associated with asthma and eosinophilia. ANCA is most frequent when glomerulonephritis is present. (Arthritis Rheum 1990;33:1094-1100)
Inclusions
- Churg-Strauss syndrome
Index Terms
Eosinophilic granulomatosis with polyangiitisAllergic granulomatous angiitisChurg-Strauss syndromeChurg-Strauss vasculitis