5A61.0

Hypopituitarism

Hipopituitarismo

Category

Definition

A disorder manifesting a deficiency or decrease of one or more pituitary hormones, which is caused by a variety of diseases such as tumour, trauma/surgery, irradiation, inflammation and haemorrhage/infarction.

Inclusions

  • pituitary cachexia
  • pituitary short stature

Index Terms

Hypopituitarismsubpituitarismhypophyseal dystrophyhypohypophysismanterior pituitary insufficiency (in part)deficient secretion of one or more pituitary hormoneshypopituitarism syndromepituitary deficiencypituitary failurepituitary hypofunctionpituitary insufficiency NOSanterior pituitary hypofunctiondeficient secretion of all pituitary hormoneshypopituitary dwarfismhyposomatotropic dwarfismhypophyseal dwarfismhypopituitary cachexiahypophyseal short staturepanhypopituitarism syndromepituitary cachexiajuvenile hypopituitarismpituitary dwarfismpituitary gland hypofunctionprimary hypopituitarismsecondary hypogonadismprepubertal panhypopituitarismprepubertal dwarfismpostpartum panhypopituitary syndromepostpartum hypopituitarismpituitary short staturepituitary infantilismpituitary hypogonadismpituitary hypoadrenocorticismNonacquired hypopituitarismNon-acquired pituitary deficiencyIsolated FSH deficiencyIsolated follicle stimulating hormone deficiencyNonacquired combined hypopituitarismNon-acquired combined pituitary deficiencyAdenohypophysis deficiency with or without pituitary stalk interruption syndrome (PSIS)PanhypopituitarismSepto-optic dysplasiaSeptooptic dysplasia spectrumDe Morsier syndromesepto-optic dysplasia sequenceSOD - [Septo-optic dysplasia]Nonacquired isolated growth hormone deficiencyCongenital isolated growth hormone deficiencyPituitary nanismCongenital IGHD - [isolated growth hormone deficiency]Growth hormone deficiency with or without pituitary stalk interruption syndromeGrowth hormone deficiency with or without PSIS - [pituitary stalk interruption syndrome]Genetic growth hormone deficiencyX-linked intellectual deficit with isolated growth hormone deficiencyIdiopathic growth hormone deficiencygrowth hormone insufficiencyisolated deficiency of growth hormoneisolated growth hormone insufficiencyisolated deficiency of [HGH] - human growth hormoneShort stature due to growth hormone qualitative anomalyNanism due to growth hormone qualitative anomalyKowarski syndromePituitary stalk interruption syndromeEctopic neurohypophysisPSIS - [pituitary stalk interruption syndrome]Short stature due to a defect in growth hormone receptor or post receptor pathwayGrowth hormone insensitivity syndromeGHIS - [Growth hormone insensitivity syndrome]Growth delay due to insulin-like growth factor I deficiencyPrimary insulin-like growth factor deficiencyGrowth delay - deafness- intellectual deficitIGF-1 - [ insulin-like growth factor I] deficiencyGrowth delay due to insulin-like growth factor I resistanceResistance to IGF-1 - [ insulin-like growth factor I]Short stature due to growth hormone resistanceComplete growth hormone insensitivityPrimary growth hormone insensitivityGrowth hormone receptor deficiencyPrimary growth hormone resistancePrimary GH resistanceLaron-type dwarfismLaron syndromeShort stature due to primary acid-labile subunit deficiencyLaron syndrome with immunodeficiencyCongenital hypogonadotropic hypogonadismAnosmic congenital hypogonadotropic hypogonadismCongenital hypogonadotropic hypogonadism with anosmiahypogonadotropic eunuchoidismanosmia eunuchoidismdysplasia olfactogenitalis of de Morsiergonadotrophin deficiency with anosmiaNormosmic congenital hypogonadotropic hypogonadismIsolated congenital gonadotropin deficiencyisolated gonadotrophin deficiencySyndrome with hypogonadotropic hypogonadismBardet-Biedl syndromeBBS - [Bardet-Biedl syndrome]Cataract - intellectual deficit - hypogonadismCHARGE syndromeColoboma, Heart defect, Atresia choanae, Retarded growth and development, Genital hypoplasia, Ear anomalies/deafnessChoanal atresia, Coloboma, Characteristic ears and Cranial nerve anomaliesCHARGE associationWoodhouse-Sakati syndromeDiabetes - hypogonadism - deafness - intellectual deficitHypogonadotropic hypogonadism associated with other endocrinopathiesAcquired hypopituitarismSecondary hypopituitarismDrug-induced hypopituitarismdrug hypopituitarismmedicament-induced hypopituitarismTumoural hypopituitarismInfectious hypopituitarismAutoimmune hypopituitarismVascular hypopituitarismSheehan syndromeSheehan diseaseHypopituitarism due to a metabolic diseaseHypopituitarism secondary to a metabolic diseaseHypopituitarism due to a granulomatous diseaseHypopituitarism secondary to a granulomatous diseaseTraumatic hypopituitarismHypophysitisLymphocytic hypophysitisGranulomatous hypophysitisIgG4-related hypophysitisXanthomatous hypophysitisPineal germinomaSuprasellar germinomaPituitary deficiency due to Rathke pouch cystsPituitary dermoid or epidermoid cystsPituitary deficiency due to empty sella turcica syndromePituitary apoplexyLate-onset isolated ACTH deficiencyLate-onset isolated adrenocorticotropin deficiencyIdiopathic hypopituitarismSimmonds SyndromeAmenorrhoea-hyperprolactinaemia syndromeBrissaud's infantilism or dwarfismFemale infertility associated with pituitary-hypothalamic originFertile eunuch syndromeInfantilism syndromeIschaemic pituitary necrosisIschaemic postpartum pituitary necrosisIsolated deficiency of pituitary hormonepituitary hormone deficiencyIsolated lutropin deficiencyIsolated luteinising hormone deficiencyIsolated somatotropin deficiencysomatotropin deficiencyLorain dwarfismLorain infantilismLorain-Levi dwarfismNecrosis of pituitary glandPostpartum pituitary necrosispostpartum necrosis of pituitary glandMyopathy in hypopituitarismOlfactogenital dysplasia