5A61.5

Central diabetes insipidus

Diabetes insipidus central

Category

Definition

Central diabetes insipidus (CDI) is a hypothalamus-pituitary disease characterised by polyuria and polydipsia due to a vasopressin (AVP) deficiency. The condition may be associated with deficient secretion of antidiuretic hormone (ADH) and is most frequently idiopathic (possibly due to autoimmune injury to the ADH-producing cells), or may be induced by trauma, pituitary surgery, or hypoxic or ischaemic encephalopathy.

Exclusions

  • Nephrogenic diabetes insipidus

Inclusions

  • ADH - [antidiuretic hormone secretion] deficiency

Index Terms

Central diabetes insipidusdiabetes insipidusDI - [diabetes insipidus]neurogenic diabetes insipidusADH - [antidiuretic hormone secretion] deficiencydiabetes mellitus insipidusfamilial diabetes insipidusantidiuretic hormone hyposecretionvasopressin deficiency syndromeprimary central diabetes insipidusvasopressin deficiencyvasopressin hyposecretiondiabetes insipidus secondary to vasopressin deficiencyWolfram syndromeDiabetes insipidus, diabetes mellitus, optic atrophy, and deafnessDIDMOAD - [Diabetes insipidus, diabetes mellitus, optic atrophy, and deafness] syndromeAcquired central diabetes insipidusAcquired central diabetes due to Infiltrative diseaseIdiopathic acquired central diabetes insipidusTraumatic central diabetes insipidusNon-acquired central diabetes insipidusCranial diabetes insipidusNeurohypophyseal diabetes insipidus