5C50.00

Classical phenylketonuria

Fenilcetonúria clássica

Category

Definition

Classical phenylketonuria is a severe form of phenylketonuria (PKU) an inborn error of amino acid metabolism characterised in untreated patients by severe intellectual deficit and neuropsychiatric complications.

Index Terms

Classical phenylketonuriaphenylpyruvic oligophreniaoligophrenia phenylpyruvicaimbecilitus phenylpyruvicaTypical phenylketonuriaphenylpyruvic aciduriaPAH - [phenylalanine hydroxylase] deficiencyhyperphenylalaninaemia Type ITypical PKU - [phenylketonuria]Folling diseaseClassical phenylketonuria, phenylalanine hydroxylase partial deficiencyClassical phenylketonuria, phenylalanine hydroxylase total deficiency