5C50.D

Disorders of branched-chain amino acid metabolism

Distúrbios do metabolismo de aminoácidos de cadeia ramificada

Category

Exclusions

  • Methylmalonic acidaemia
  • Propionic acidaemia
  • Isovaleric acidaemia
  • 3-methylglutaconic aciduria
  • Developmental delay due to 2-methylbutyryl-CoA dehydrogenase deficiency
  • 3-hydroxyisobutyric aciduria

Subcategories (1)