5C52.02

Disorders of ketone body metabolism

Distúrbios do metabolismo de corpos cetônicos

Category

Index Terms

Disorders of ketone body metabolism3-hydroxy 3-methylglutaryl-CoA lyase deficiency3-hydroxy 3-methylglutaryl-CoA synthase deficiencyHMG-CoA lyase deficiencyHMG-CoA synthase deficiencySuccinyl-CoA acetoacetate transferase deficiencySuccinyl-CoA:3-ketoacid CoA transferase (SCOT) deficiency