5D00.0
AL amyloidosis
Amiloidose de Cadeia Leve de Imunoglobulina
CategoryDefinition
AL amyloid is due to the deposition of immunoglobulin light chains in glomeruli where they are seen as Congo red binding fibrils and immuno-stain specifically for kappa or lambda light chains. By light microscopy there is amorphous hyaline material in the mesangium and capillary walls. A light chain producing plasma cell or B-cell dysplasia is responsible. Other organs are also involved in this systemic disease.
Index Terms
AL amyloidosisPrimary amyloidosisImmunoglobulinic amyloidosisAmyloid ALOrgan-limited amyloidosisAD type amyloidosislocalised amyloid depositlocalised amyloidosislocalised amyloid infiltrationlocalised primary amyloidosislocalised generalised amyloid infiltrationlocalised generalised amyloidosisCardiac organ-limited amyloidosisfamilial amyloid cardiomyopathyamyloid cardiomyopathyamyloid heartamyloid heart degenerationamyloid heart diseaseamyloid heart muscle diseasecardiac amyloidosissenile cardiac amyloidosisheart amyloidosisfamilial amyloid heart diseaseDanish type familial amyloid cardiomyopathyGlomerular disorders in organ-limited amyloidosisamyloid nephritisnephrotic syndrome in amyloidosisAmyloidosis of liverhepatic amyloidosisAmyloidosis of small intestineAmyloid gastrointestinal diseaseamyloid intestinal degenerationPrimary localised cutaneous amyloidosisMacular amyloidosisPapular amyloidosisLichen amyloidosisNodular amyloidosisAmyloidosis cutis nodularis atrophicansTumefactive amyloidosisInterstitial lung diseases associated with amyloidosispulmonary amyloidosisHepatic amyloidosis with intrahepatic cholestasisCholestatic hepatic amyloidosisArthropathy in amyloidosisamyloid arthropathyamyloid arthritisarticular amyloidarthritis secondary to amyloidosisGlaucoma in amyloidosisAmyloid spinal degenerationAmyloid splenic degenerationamyloid splenic diseaseAS transthyretin amyloidosisDanish type amyloidosisDenmark type amyloidosisALECT2 amyloidosis