6D80.0
Dementia due to Alzheimer disease with early onset
Demência devida à doença de Alzheimer com início precoce
CategoryDefinition
Dementia due to Alzheimer disease in which symptoms emerge before the age of 65 years. It is relatively rare, representing less than 5% of all cases, and may be genetically determined (autosomal dominant Alzheimer disease). Clinical presentation may be similar to cases with later onset, but progression of cognitive deficits may be more rapid.
Coding Note
This category should never be used in primary tabulation. The codes are provided for use as supplementary or additional codes when it is desired to identify the presence of dementia in diseases classified elsewhere.
When dementia is due to multiple aetiologies, code all that apply.
Diagnostic Criteria
- All diagnostic requirements for Dementia Due to Alzheimer Disease are met.
- Neurocognitive, functional, and or behavioural symptoms associated with Alzheimer Disease were present prior to age 65, as evidenced by neuropsychological test data, neuroimaging data, genetic testing, medical tests, family history, and/or clinical history.
Index Terms
Dementia due to Alzheimer disease with early onsetAlzheimer type presenile dementiaearly onset Alzheimer dementiadementia in Alzheimer disease type 2dementia in Alzheimer disease with early onsetearly onset Alzheimer type dementia, uncomplicatedprimary degenerative Alzheimer type dementia, early onsetprimary degenerative Alzheimer type dementia, presenile onset, uncomplicatedAlzheimer disease dementia with early onsetpresenile sclerosispresenile brain sclerosispresenile Alzheimer brain sclerosisAutosomal dominant Alzheimer disease dementia, mutation of presenilin 1Autosomal dominant Alzheimer disease dementia, mutation of presenilin 2Autosomal dominant Alzheimer disease dementia, mutation of amyloid precursor protein