8B22.3

Isolated cerebral amyloid angiopathy

Angiopatia amiloide cerebral isolada

Category

Definition

Cerebral amyloid angiopathy is characterised by the progressive accumulation of amyloid protein in the walls of small-to-medium-sized arteries and arterioles predominantly located in the leptomeningeal space, the cortex, and, to a lesser extent, also in the capillaries and veins.

Index Terms

Isolated cerebral amyloid angiopathyCAA - [cerebral amyloid angiopathy]cerebrum amyloid angiopathycongophilic angiopathyFamilial dementia, British typeFamilial dementia, Danish typeHereditary amyloid precursor protein angiopathyHereditary cerebral haemorrhage with amyloidosis, Dutch typeHereditary cerebral haemorrhage with amyloidosis, Icelandic typeHereditary cystatin C amyloid angiopathySporadic amyloid angiopathy