8B60.3
Progressive muscular atrophy
Atrofia muscular progressiva
CategoryDefinition
In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles are present without upper motor neuron involvement. Over time, some patients may progress to develop upper motor neuron signs, of which pathological evidence is common even in patients who never displayed clinical upper motor neuron signs, suggesting that progressive muscular atrophy is a form of ALS.
Exclusions
- Fazio-Londe syndrome
- Amyotrophic lateral sclerosis
Index Terms
Progressive muscular atrophyhereditary spinal muscle atrophyPMA - [progressive muscular atrophy]progressive muscle atrophyprogressive spinal muscle atrophypure progressive muscular atrophyDuchenne-Aran atrophyDuchenne-Aran muscle atrophyhereditary SMA - [spinal muscle atrophy]