8C21.2
Hereditary sensory and autonomic neuropathy type IV
Neuropatia hereditária sensitiva e autonômica tipo IV
CategoryDefinition
Hereditary sensory and autonomic neuropathy, type 4 (HSAN4) is an inherited disorder characterised by anhidrosis, insensitivity to pain, self-mutilating behaviour and episodes of fever.
Index Terms
Hereditary sensory and autonomic neuropathy type IVCongenital insensitivity to pain with anhidrosisHSAN4 - [Hereditary sensory and autonomic neuropathy type 4]