8C72.00

Nemaline myopathy

Miopatia nemalínica

Category

Definition

Nemaline myopathy encompasses a large spectrum of congenital myopathies characterised by hypotonia, weakness and depressed or absent deep tendon reflexes, with pathologic evidence of nemaline bodies (rods) on muscle biopsy.

Index Terms

Nemaline myopathyrod myopathynemaline body diseaseAdult-onset nemaline myopathyAmish nemaline myopathyIntermediate nemaline myopathyMild nemaline myopathySevere congenital nemaline myopathyTypical nemaline myopathy