8C74

Periodic paralyses or disorders of muscle membrane excitability

Paralisias ou transtornos de excitabilidade da membrana muscular periódicos

Category

Definition

These are a group of disorders caused by malfunctioning of the ion channels in skeletal muscle membranes causing the cells to depolarize leading to weakness or paralysis. The common triggers include cold, heat, high carbohydrate meals, stress, excitement, physical exertion etc.

Diagnostic Criteria

Signs & symptoms Variable depending on the type. These are caused by mutations in various ion channels including sodium, potassium, or chloride, and thus, are referred as muscle channelopathies.

Subcategories (2)