8D84

Pure autonomic nervous system failure

Insuficiência autonômica pura

Category

Definition

Pure autonomic failure is a sporadic, adult onset, slowly progressive disorder associated with accumulation of synuclein in peripheral autonomic neurons resulting in orthostatic hypotension, bladder and sexual dysfunction.

Index Terms

Pure autonomic nervous system failureIdiopathic orthostatic hypotensionBradbury-Eggleston syndrome