BC65.5
Catecholaminergic polymorphic ventricular tachycardia
Taquicardia ventricular polimórfica catecolaminérgica
CategoryDefinition
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death.
Index Terms
Catecholaminergic polymorphic ventricular tachycardiaCatecholaminergic polymorphic ventricular tachycardia due to RYR2 mutationCatecholaminergic polymorphic ventricular tachycardia due to Calsequestrin mutation