BD93.0
Primary lymphoedema
Linfedema primário
CategoryDefinition
Lymphoedema as a result of lymphatic vessel hypoplasia
Index Terms
Primary lymphoedemaCongenital lymphoedemaSimple primary lymphoedemaCongenital primary lymphoedemaMilroy diseaseHereditary lymphoedema type I: (MIM 153100)Peripubertal primary lymphoedemaMeige diseaseHereditary lymphoedema type II: (MIM153200)Lymphoedema praecoxSporadic late-onset primary lymphoedemaComplex primary lymphoedemaLymphoedema with atrial septal defects and facial changesLymphoedema-distichiasis syndromeLDS - [lymphoedema distichiasis syndrome] (MIM 153400)Hennekam lymphangiectasia-lymphoedema syndromeLymphoedema, microcephaly and chorioretinopathy syndromeDeafness, lymphoedema and leukaemia syndromeEmberger syndrome