CB04.31
Pulmonary alveolar proteinosis
Proteinose alveolar pulmonar
CategoryDefinition
This is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia), pulmonary infection, or environmental exposure to dusts or chemicals.
Index Terms
Pulmonary alveolar proteinosisAutoimmune pulmonary alveolar proteinosisIdiopathic pulmonary alveolar proteinosisIdiopathic alveolar lipoproteinosisCongenital pulmonary alveolar proteinosisSecondary pulmonary alveolar proteinosis