DC33
Autoimmune pancreatitis
Pancreatite autoimune
CategoryDefinition
Autoimmune pancreatitis (AIP) is a rare pancreatic disease characterised by chronic non-alcoholic pancreatitis that presents with abdominal pain, steatorrhoea, obstructive jaundice and responds well to steroid therapy and is seen in two subforms: type 1 AIP which affects elderly males, involves other organs and has increased immunoglobin G4 (IgG4) levels and type 2 AIP which affects both sexes equally but presents at a younger age and has no other organ involvement or increased IgG4 levels.
Index Terms
Autoimmune pancreatitisType 1 IgG4 related autoimmune pancreatitisLPSP - [lymphoplasmacytic sclerosing pancreatitis]Autoimmune pancreatitis with other organ involvementAutoimmune pancreatitis without other organ involvementType 2 Autoimmune pancreatitis featuring granulocytic epithelial lesionIDCP - [idiopathic duct-centric chronic pancreatitis]Type 2 Autoimmune pancreatitis featuring GEL