EA94
Pityriasis rubra pilaris
Pitiríase rubra pilar
CategoryDefinition
Pityriasis rubra pilaris (PRP) is the name given to a group of clinically similar papulosquamous dermatoses of unknown aetiology. They initially present with erythematous, hyperkeratotic perifollicular papules, which tend to coalesce into plaques, but may progress to erythroderma, particularly in adults. The distribution, age of onset and speed of onset differ markedly between patients and these differences have been used to classify PRP into a number of clinically distinct subtypes.
Index Terms
Pityriasis rubra pilarisPRP - [pityriasis rubra pilaris]Devergie's diseasePityriasis rubra pilaris, adultPityriasis rubra pilaris type I, classical adultPityriasis rubra pilaris type II, atypical adultPityriasis rubra pilaris, juvenilePityriasis rubra pilaris type III, classical juvenilePityriasis rubra pilaris type IV, circumscribed juvenilePityriasis rubra pilaris type V, atypical juvenileHIV-associated pityriasis rubra pilaris