EC20.02

Autosomal recessive congenital ichthyosis

Ictiose congênita autossômica recessiva

Category

Definition

A heterogeneous group of genetically-determined ichthyoses with autosomal recessive inheritance.

Index Terms

Autosomal recessive congenital ichthyosisCongenital non-bullous ichthyosiform erythrodermaCongenital ichthyotic ichthyosisLamellar ichthyosisCollodion babyCongenital lamellar ichthyosisHarlequin ichthyosisHarlequin colour change syndromeSelf-healing collodion babyAcral self-healing collodion babyBathing suit ichthyosis