EC20.2
Hereditary acantholytic dermatoses
Dermatoses acantolíticas hereditárias
CategoryDefinition
A group of heritable disorders characterised by epidermal acantholysis and loss of epidermal integrity.
Inclusions
- Darier disease
- Hailey-Hailey disease
Index Terms
Hereditary acantholytic dermatosesDarier diseaseDarier disease (MIM 124200)Keratosis follicularisDarier-White diseaseDyskeratosis follicularisAcrokeratosis verruciformis of DarierHailey-Hailey diseaseBenign familial pemphigusGougerot-Hailey-Hailey disease