EC20.30
Diffuse palmoplantar keratodermas
Ceratodermias palmoplantares difusas
CategoryDefinition
Palmoplantar keratoderma in which there is confluent epidermal thickening affecting the palms and soles.
Index Terms
Diffuse palmoplantar keratodermasNon-syndromic diffuse palmoplantar keratodermasDiffuse epidermolytic palmoplantar keratodermaVörner-Thost palmoplantar keratodermaDiffuse non-epidermolytic palmoplantar keratodermaUnna palmoplantar keratodermaTylosisMal de MeledaKeratosis palmoplantaris transgrediens of SiemensMeleda disease (OMIM #248300)Nagashima-type palmoplantar keratodermaKeratolytic winter erythemaOudtshoorn diseaseSyndromic diffuse palmoplantar keratodermasPapillon-Lefèvre syndromeCathepsin C deficiencyCongenital palmoplantar or perioral keratodermaOlmsted syndromeCurly hair – acral keratoderma – caries syndromeCHACS - [Curly hair – acral keratoderma – caries syndrome]CHAC syndrome - [Curly hair - acral keratoderma - caries] syndromePalmoplantar keratoderma with scleroatrophy of the extremitiesHuriez palmoplantar keratodermaPalmoplantar keratoderma-sclerodactyly syndromeSclerotylosisConnexin palmoplantar keratoderma with sensorineural deafnessCicatrizing palmoplantar keratoderma with hearing loss (Vohwinkel)Vohwinkel keratoderma (MIM 124500)Congenital deafness with keratopachydermia or constrictions of fingers or toesLoricrin palmoplantar keratoderma with ichthyosisVohwinkel syndrome - ichthyosisKeratoderma hereditarium mutilans - ichthyosisMutilating keratoderma with ichthyosisPalmoplantar keratoderma – digital clubbing – acro-osteolysisBureau-Barrière-Thomas palmoplantar keratoderma