EF40.10

Urticarial vasculitis

Vasculite urticariforme

Category

Definition

An uncommon form of cutaneous leucocytoclastic vasculitis manifested by urticarial weals which, in contrast to those of chronic urticaria, are long-lasting and painful rather than itchy. A cause is often not identified. It may be associated with hypocomplementaemia and systemic inflammation (hypocomplementaemic urticarial vasculitis).

Index Terms

Urticarial vasculitisNormocomplementaemic urticarial vasculitis