FB86.10
Hypertrophic osteoarthropathy
Osteoartropatia hipertrófica
CategoryDefinition
Hypertrophic osteoarthropathy (HOA) is a syndrome of clubbing of the digits, subperiosteal new bone formation (periostitis) affecting the long bones, and arthritis. The primary hereditary form is associated with mutations in the HPGD gene. The secondary form may be secondary to a number of systemic disorders, most commonly as a paraneoplastic phenomenon related to bronchial carcinoma.
Exclusions
- Isolated congenital club finger
Index Terms
Hypertrophic osteoarthropathyBamberger-Marie syndromeMarie-Bamberger diseasePierre-Marie-BambergerPrimary hypertrophic osteoarthropathyCranio-osteoarthropathyPachydermoperiostosisTouraine-Solente-Gole syndromeClubbed nail pachydermoperiostosisSecondary hypertrophic osteoarthropathyParaneoplastic hypertrophic osteoarthropathyHypertrophic pulmonary osteoarthropathy