LA75.4
Congenital pulmonary airway malformations
Malformações congênitas das vias aéreas pulmonares
CategoryDefinition
A disease caused by failure of the bronchial structure to correctly develop during the antenatal period. This disease may present with severe respiratory distress in the newborn period, acute respiratory distress or infection later in life, or may be asymptomatic. This disease can be distinguished from other lesions and normal lung by polypoid projections of the mucosa, an increase in smooth muscle and elastic tissue within the cyst walls, an absence of cartilage in the cystic parenchyma, mucous secreting cells, and the absence of inflammation.
Exclusions
- Cystic lung disease, acquired or unspecified
Inclusions
- Congenital honeycomb lung
- Congenital polycystic disease of lung
Index Terms
Congenital pulmonary airway malformationsCongenital cystic disease of lungCongenital lung cystCongenital cystic lungCongenital cystic adenomatoid malformationCCAM - [Congenital cystic adenomatoid malformation]Congenital polycystic disease of lungCongenital polycystic lungMultiple congenital bronchogenic cystsCongenital honeycomb lungCongenital pulmonary airway malformation type 0CPAM type 0 - [Congenital pulmonary airway malformation type 0]Congenital pulmonary airway malformation type 1CPAM type 1 - [Congenital pulmonary airway malformation type 1]Congenital pulmonary airway malformation type 2CPAM type 2 - [Congenital pulmonary airway malformation type 2]Congenital pulmonary airway malformation type 3CPAM type 3 - [Congenital pulmonary airway malformation type 3]Congenital pulmonary airway malformation type 4CPAM type 4 - [Congenital pulmonary airway malformation type 4]