LA8A.23

Aortic valvar atresia

Atresia valvar aórtica

Category

Definition

A congenital cardiovascular malformation in which there is no orifice of the aortic valve. Additional information: aortic valvar atresia will most often not be coded independently, as it is frequently included within the 'Hypoplastic left heart syndrome' code as part of this spectrum of cardiovascular malformations. However, there is a small subset of patients with aortic valve atresia who have a well developed left ventricle and mitral valve and a large ventricular septal defect (nonrestrictive or restrictive).

Coding Note

Aortic valve atresia will most often be coded under the hypoplastic left heart syndrome/complex diagnostic codes since it most often occurs as part of a spectrum of cardiovascular malformations. However, there is a small subset of patients with aortic valve atresia who have a well developed left ventricle and mitral valve and a large ventricular septal defect (nonrestrictive or restrictive).

Index Terms

Aortic valvar atresiaaortic valve atresiaaortic valvular atresiacongenital atresia of aortic valveimperforate aortic valve