LB22.0
Congenital asplenia
Asplenia congênita
CategoryDefinition
A condition caused by failure of the spleen to develop during the antenatal period. This condition may present with pneumococcal sepsis. Confirmation is through verification of no spleen by imaging.
Index Terms
Congenital aspleniaCongenital absent spleenCongenital splenic absenceCongenital absence of spleenAplasia of spleenCongenital aplasia of spleenSpleen agenesis