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Bent bone dysplasias

Displasias de ossos encurvados

Category

Definition

Any syndromes are characterised by poor mineralization of the skull, craniosynostosis, hypoplastic pubis and clavicles, osteopenia, bent long bones, low-set ears, hypertelorism, midface hypoplasia, prematurely erupted fetal teeth, and micrognathia. These syndromes may be associated with mutation of the FGFR2 gene.

Index Terms

Bent bone dysplasiasStüve-Wiedemann syndromeKyphomelic dysplasiaCampomelia, Cumming typeWeismann-Netter syndrome