LD27.01

Cronkhite-Canada syndrome

Síndrome de Cronkhite-Canadá

Category

Definition

Cronkhite-Canada syndrome (CCS) is a sporadically occurring, noninherited disorder of generalised gastrointestinal polyps (hamartomas), cutaneous pigmentation, alopecia, and onychodystrophy. The possibility of progression to cancer is considered to be low. Chronic diarrhea and protein-losing enteropathy are often observed.

Index Terms

Cronkhite-Canada syndrome