4A01.0
Immunodeficiencies with predominantly antibody defects
Imunodeficiências com predominância de defeitos de anticorpos
CategoryDefinition
A disorder characterised by an inability to mount a normal immune response due to antibody (i.e. immunoglobulin) defects
Subcategories (6)
4A01.00Hereditary agammaglobulinaemia with profoundly reduced or absent B cells4A01.01Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells4A01.02Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells4A01.03Transient hypogammaglobulinaemia of infancy4A01.04Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells4A01.05Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells